Loeys-Dietz syndrome with bilateral radial head dislocations: a case report.
نویسندگان
چکیده
Loeys-Dietz syndrome is characterised by vascular aneurysms, hypertelorism, and a bifid uvula. We report on an 11-year-old boy with Loeys-Dietz syndrome who presented with bilateral radial head dislocations and severe osteopaenia with changes of avascular necrosis in both hips causing an out-toeing, wide gait. Considering the poor prognosis for elbow movement and possible radial head dysplasia, surgical reduction of the radial heads was deferred. A subtrochanteric de-rotation osteotomy of the left hip was performed to improve the gait.
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ورودعنوان ژورنال:
- Journal of orthopaedic surgery
دوره 21 2 شماره
صفحات -
تاریخ انتشار 2013